Systemic vasculitis

Necrotizing vasculitis also called Systemic necrotizing vasculitus (SNV) is a category of vasculitis, comprising vasculitides that present with necrosis. Necrotizing vasculitis also called Systemic necrotizing vasculitus (SNV) is a category of vasculitis, comprising vasculitides that present with necrosis. Examples include giant cell arteritis, microscopic polyangiitis, and granulomatosis with polyangiitis. ICD-10 uses the variant 'necrotizing vasculopathy'. ICD-9, while classifying these conditions together, doesn't use a dedicated phrase, instead calling them 'polyarteritis nodosa and allied conditions'. When using the influential classification known as the 'Chapel Hill Consensus Conference', the terms 'systemic vasculitis' or 'primary systemic vasculitides' are commonly used. Although the word 'necrotizing' is omitted, the conditions described are largely the same. Giant-cell arteritis and Takayasu's arteritis have much in common, but usually affect patients of different ages, with Takayasu's arteritis affecting younger people, and giant-cell arteritis having a later age of onset. Aortitis can also be considered a large-vessel disease. Takayasu arteritis. Primarily affects the aorta and its main branches. At least 3 out of 6 criteria yields sensitivity and specificity of 90.5 and 97.8%: Giant cell (temporal) arteritis. Chronic vasculitis of both large and medium vessels, primarily affecting cranial branches of the arteries arising from the aortic arch. At least 3 out of 5 criteria yields sensitivity and specificity of 95 and 91%: These conditions are sometimes considered together with the small vessel vasculitides.