Keratosis follicularis spinulosa decalvans

Keratosis follicularis spinulosa decalvans is a rare X-linked disorder described by Siemens in 1926, a disease that begins in infancy with keratosis pilaris localized on the face, then evolves to more diffuse involvement.:580,762:649,714 Keratosis follicularis spinulosa decalvans is a rare X-linked disorder described by Siemens in 1926, a disease that begins in infancy with keratosis pilaris localized on the face, then evolves to more diffuse involvement.:580,762:649,714 An association with SAT1 has been suggested.

[ "Scalp", "Hyperkeratosis", "Scarring alopecia", "Keratosis pilaris atrophicans", "Keratosis pilaris atrophicans faciei" ]
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