Angiolymphoid hyperplasia with eosinophilia (also known as: 'Epithelioid hemangioma,' 'Histiocytoid hemangioma,' 'Inflammatory angiomatous nodule,' 'Intravenous atypical vascular proliferation,' 'Papular angioplasia,' 'Inflammatory arteriovenous hemangioma,' and 'Pseudopyogenic granuloma') usually presents with pink to red-brown, dome-shaped, dermal papules or nodules of the head or neck, especially about the ears and on the scalp. Angiolymphoid hyperplasia with eosinophilia (also known as: 'Epithelioid hemangioma,' 'Histiocytoid hemangioma,' 'Inflammatory angiomatous nodule,' 'Intravenous atypical vascular proliferation,' 'Papular angioplasia,' 'Inflammatory arteriovenous hemangioma,' and 'Pseudopyogenic granuloma') usually presents with pink to red-brown, dome-shaped, dermal papules or nodules of the head or neck, especially about the ears and on the scalp. It, or a similar lesion, has been suggested as a feature of IgG4-related skin disease, which is the name used for skin manifestations of IgG4-related disease.