Xanthomatose normolipidemique a localisation nasale chez une patiente de 18 ans
2012
Introduction : Exposer un cas de xanthomatose normolipidemique. Observation : il s’agit d’une adolescente de 18 ans qui a presente une masse des cavites nasales dont le bilan paraclinique a plaide en faveur d’un xanthogranulome juvenile. L’evolution a court terme a ete satisfaisante apres l’exerese chirurgicale par une voie combinee externe et endonasle. Conclusion : il s’agit d’une presentation inhabituelle de la xanthomatose dont les difficultes diagnostiques d’ordre multifactoriel, ont ete relevees. Mots cles : Cavites nasales – Xanthomatoses –granulomatoses chroniques Introduction : To expose a case of normolipidemic xanthomatosis Case report : An 18 years aged girl has presented a swelling involving the nasal cavities. Paraclinical examens have evoked a case of juvenile xanthogranuloma. Earlier outcome was good after a surgical removal which has combined external and endonasal way. Conclusion : it’s an unusual feature of xanthomatis. The difficulties of diagnosis which seemed caused by many factors have been point out. Keyswords : Nasal cavities – Xanthomatosis – Chronic granuloma
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