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Doença de Madelung: relato de caso

2010 
Doenca de Madelung ou lipomatose benigna multipla simetrica e uma doenca rara, caracterizada pelo acumulo de gordura nao encapsulada, geralmente localizada simetricamente ao redor do pescoco, ombros, regiao subociptal e no torax. A etiologia e desconhecida, entretanto, frequentemente e observada em pacientes com historia de alcoolismo cronico acompanhada de alteracoes metabolicas. Os autores apresentam um caso de lipomatose cervical associada a polineuropatia e ao alcoolismo. A remocao cirurgica do tecido adiposo por lipectomia ou lipoaspiracao e terapia paliativa, pois a recorrencia e comum. Madelung's disease or multiple symmetric lipomatosis is a rare disease characterized by non-encapsulated accumulation of fat, generally located symmetrically on cervical area, shoulders, suboccipital area and trunk. The etiology is unknown, but is often observed in patients with a history of chronic alcoholism and it is accompanied by metabolic abnormalities. The authors present a case of lipomatosis. The treatment is palliative associated with the removal of excessive fat tissue by lipectomy or liposuction, and the recurrence is common.
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