Tortícolis paroxístico benigno infantil (TPBI)

espanolEl torticolis paroxistico benigno de la infancia(TPBI) es una enfermedad benigna, rara y sorprendente, que se caracteriza por episodios recurrentes de inclinacion lateral de la cabeza en ninos pequenos. Se trata de una patologia posiblemente infradiagnosticada, pero que por lo alarmante que puede resultar alguno de sus sintomas suele conllevar la practica de multiples exploraciones. Con el proposito de difundir entre nosotros su conocimiento, lo ilustramos con 2 casos clinicos. Descripcion: Se trata de dos ninos que hacia los 2 anos comienzan a desarrollar el TPBI. Su evolucion fue benigna, el diagnostico se obtuvo tras la negatividad de las exploraciones complementarias y en ambos detectamos el antecedente de migranas familiares. Discusion: El diagnostico del TPBI es clinico, aunque la presencia de sintomas anadidos, tales como vomitos, palidez, movimientos oculares, etc., y su escasa frecuencia, suelen incrementar las dificultades diagnosticas. La etiologia es discutida pero la fisiopatologia se supone que guarda estrecha relacion con los sindromes periodicos de la infancia, formando parte de los equivalentes migranosos. Conclusion: El conocimiento de esta patologia es la mejor manera de diagnosticarla, pues su manejo es fundamentalmente clinico. Aunque no haya tratamiento para las crisis ni para su prevencion, deberemos tranquilizar a los padres, explicandoles el caracter benigno y autolimitado del proceso, a pesar de su recurrencia EnglishBenign paroxysmal torticollis of infancy (BPTI) is a rare and surprising benign disease, characterized by recurrent episodes of lateral tilt of the head, in young children. It's an uncommon pathology, possibly under-­diagnosed, but by the alarming that some of your symptoms can be, often lead to the practice of multiple explorations. With the purpose of spreading knowledge among us, we present 2 clinical cases. Clinical case: to illustrate this process we refer the clinic of 2 boys which began to develop the BPTI towards the age of 2 years. Its evolution was benign, the diagnosis was obtained after the negativity of the complementary examinations and both detect the common history of migraines in the family. Discussion: The diagnosis of the BPTI is clinical, but the presence of additional symptoms, such as vomiting, pallor, eye movements;; and her low frequency, tend to increase the diagnostic difficulties. Its etiology is discussed, but the pathophysiology is supposed that you linked childhood periodic syndromes, forming part of the migraine equivalents. Conclusion: We believe that knowing this pathology is the best way to diagnose it, because its management is mainly clinical. Although there is no treatment for attacks or for their prevention, we have to reassure parents, explaining the benign and self-­limiting character of the process, despite its recurrence.