Arrhythmogenic Right Ventricular Cardiomyopathy: A Case Report and Review of the Literature

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a myocardial disease primarily affecting the right ventricle (RV) and is pathologically characterized by the replacement of myocardial tissue with fatty and fibrous tissues. ARVC is a rare but important disease because of its association with sudden arrhythmic death in young and otherwise healthy people. We report on a 42-year-old man who presented with sudden onset of palpitations. His electrocardiogram (ECG) revealed sustained ventricular tachycardia (VT) with left-bundle branch block (LBBB) morphology. The VT reverted to a sinus rhythm following intravenous amiodarone administration. A sinus 12-lead ECG revealed an inverted T wave in the V1 to V3 leads. Cardiac catheterization showed normal coronary arteries and a dilated hypokinetic RV. A clinical diagnosis of ARVC was confirmed by magnetic resonance imaging (MRI) which showed a thin and dilated RV with a hyperintense signal intheRV freewall suggestive of fatty replacement. The patientwas discharged with a normal sinus rhythm on 200 mg/day amiodarone, and there was no recurrent ventricular tachycardia during a follow-up period of 12 months.