Extramammary Paget’s Disease

Extramammary Paget’s disease (EMPD) is a rare intraepithelial malignancy that has only been a few hundred times in the literature with level 4 evidence. The precise incidence is unknown. However, little is known regarding optimal treatment and prognostic factors. Due to poor understanding of the condition, it can remain undiagnosed for a number of years prior to treatment, and with individual patient numbers remaining small across centers, it becomes difficult to build up a true understanding of the disease process.