Meningioma intraóseo primario osteolítico del hueso occipital

2015 
espanolLos meningiomas intraoseos primarios son considerados meningiomas extradurales siempre que no tengan relacion con la duramadre. La mayoria crecen de huesos del craneo, pudiendo ser osteoblasticos u osteoliticos. Estos ultimos son los mas raros, habiendo muy pocos casos descritos en la literatura. Con mayor frecuencia tienen signos de malignidad, por lo que es importante el diagnostico histologico precoz de una lesion osteolitica craneal para su correcto tratamiento. El tratamiento debe ser la cirugia, con reseccion completa siempre que se pueda. Presentamos el caso de un gran meningioma intraoseo primario osteolitico del hueso occipital tratado quirurgicamente mediante craniectomia y sin signos de recidiva a los 5 anos de seguimiento. EnglishPrimary intraosseous meningiomas are considered extradural meningiomas when no dural attachment is present. Most of them arise from the cranial bones and can present either as an osteoblastic or an osteolytic lesion. Osteolytic intraosseous meningiomas are the rarest and very few cases have been reported. Given that many of these may develop signs of malignancy, early histological confirmation is important in order to ensure appropriate treatment. The recommended therapy is surgery, with complete resection whenever possible. We present the case of a large primary intraosseous osteolytic meningioma within the occipital bone, which was completely excised five years ago, currently presenting no signs of recurrence.
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