Hemorragia digestiva alta en paciente con neurofibromatosis de von Recklinghausen

Neurofibromatosis (Von Recklinghausen's disease) is unherited as an autosomal dominant trait. lt is characterised by the development of tumors in diverse sites, wich may be benign or malignant. The case of a 39 year old woman with Von Recklinghausen's disease is discussed. She presented wich a 3 year history of episodes of melaena and iron deficient anaemia. Mesenteric angiography demonstrated a hypervascular tumour in the jejunum. lt was surgically excised with an anatomopathological diagnosis of neurofibroma.