Echocardiographic Detection of Supravalvular Aortic Stenosis

The echocardiographic features of supravalvular aortic stenosis of the segmental or hourglass variety is described for the first time. Utilizing a strip recorder and an M mode or sector scan the diameter of the aortic lumen is demonstrated to narrow at the stenotic area just distal to the aortic valve. As the transducer sweeps further cephalad the aortic root lumen widens to a normal diameter.