İniensefali. Olgu sunumu

Iniencephaly is a rare but almost always lethal neural tube defect with following cardinal features: Occipithal bone defect, partial or total absence of cervicothoracal vertebrae and fetal retroflexion.There is a defect in closure of the neural tube, which, under normal circumstances, is completely fused by 28 days of gestation. Iniencephaly is associated with malformations of central nervous system, gastrointesinal - and cardiovaskuler system. We present an iniencephalic newborn with a review of literature.