A Case of von Recklinghausen's Disease with Bilateral Pheochromocytoma-Malignant Peripheral Nerve Sheath Tumors of the Adrenal and Gastrointestinal Autonomic Nerve Tumors

A 48-year-old man with neurofibromatosis type 1 presented with chest pain, paroxysmal hypertension, tachycardia, and progressive respiratory insufficiency. Clinical investigation displayed calcified tumors in the anterior mediastinum and pararenal region. Histological examination at autopsy revealed