Síndrome de Bazex asociado a carcinoma de orofaringe: descripción de un caso

2019 
espanolIntroduccion y objetivo: el sindrome de Bazex es un cuadro paraneoplasico infrecuente que se asocia generalmente a carcinoma epidermoide de via aerodigestiva superior. Se presenta un caso de Sindrome de Bazex caracteristico para contribuir a un diagnostico precoz de la patologia tumoral subyacente asociada. Descripcion del caso: varon de 57 anos, fumador y bebedor importante, que acude a consulta por tumor laterocervical izquierdo de meses de evolucion asociado a eccema descamativo y violaceo en manos, pies, pabellones auriculares y rodillas. Tras exploracion y pruebas complementarias se establece el diagnostico de carcinoma epidermoide amigdalar T2N3M0 y sindrome paraneoplasico asociado. Conclusiones: El carcinoma de orofaringe constituye uno de los tumores mas frecuentes asociados a sindrome de Bazex. Por tanto, ante esta manifestacion cutanea, siempre debemos descartar patologia oncologica a dicho nivel. EnglishIntroduction and objective: Bazex syndrome is an infrequent paraneoplastic syndrome that is related to an upper aerodigestive epidermoid carcinoma. A case of characteristic Bazex syndrome is presented to contribute to an early diagnosis of the associated underlying tumor pathology. Case description: 57-year-old male, smoker and regular drinker, presented with a cervical mass associated with scaly and violaceous eczema on hands, feet, ears and knees. After examination and complementary tests, the diagnosis of T2N3M0 tonsillar squamous cell carcinoma and paraneoplastic syndrome was established. Conclusions: Oropharyngeal carcinoma is one of the most frequent tumors associated with Bazex syndrome. Therefore, if we observe these skin lesions, we should always rule out oncological pathology at that level.
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