Camptodactyly Arthropathy Coxa Vara Pericarditis Syndrome A Report of Two Cases in Syria

2019 
Camptodactyly-arthropathy-coxa vara-pericarditis Syndrome (CACP) is a rare condition presents with camptodactyly, non-inflammatory arthropathy, progressive coxa vara and occasionally non inflammatory pericarditis. CACP syndrome can be diagnosed at birth or during early childhood. At first, CACP syndrome may be confused with juvenile idiopathic arthritis (JIA) because both diseases have similar symptoms. The treatment options for both diseases are different which makes the distinction between the two of high importance. We present a case two cases of CACP syndrome in two female sibling’s sisters with healthy consanguineous parents that has have distinctive radiological and histological evidence of this rare condition. The younger one presented with camptodactyly, flexion contracture of the fingers with restricted motions, swollen joints and gait disturbance.
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