A rare case of biventricular non-compaction associated with ventricular septal defect and descendent aortic stenosis in a young man

Noncompaction of the ventricular myocardium is a cardiomyopathy caused by the arrest of normal embryogenesis of the ventricles. It is classified in isolated noncompaction of the ventricles (most frequently of the left one) and in ventricular noncompaction associated with other congenital anomalies of the endocardium and myocardium, such as obstruction of the right or left ventricular outflow tracts, complex cyanotic congenital heart disease, and coronary artery anomalies. There are controversies regarding the right ventricle noncompaction due to the normally trabeculated shape of its walls.We present a case of severe heart failure with a complex anomaly: biventricular noncompaction, ventricular septal defect and aortic thoracic stenosis.