IgG4-associated Cholangitis Mimicking Cholangiocarcinoma-Report of a Case

Immunoglobulin G4 (IgG4)-associated cholangitis is a novel clinicopathological disease entity. It was formerly recognized as one of extrapancreatic diseases of autoimmune pancreatitis. Now, it is redesignated as one of the IgG4-associated sclerosing diseases, which are characterized by high serum IgG4 concentrations and extensive infiltration of IgG4-positive plasma cells into the involved organs. We described a case of obstructive jaundice had a clinical presentation resembling cholangiocarcinoma proved to be IgG4-associated cholangitis after surgery.