Paraneoplastic pemphigus with anti-BP180 autoantibodies and Castleman's disease.

Paraneoplastic pemphigus (PNP) is commonly associated with IgG-autoantibodies against desmoglein 1 and 3, plakins (desmoplakin I and II, envoplakin, periplakin), desmocollins 1-3, BP2301 and α2-macroglobulin-like-1 (A2ML1)2. The major autoantigen of bullous pemphigoid (BP), pemphigoid gestationis and lichen planus pemphigoides (LPP) is the NC16A domain of BP1803. This article is protected by copyright. All rights reserved.