Síndrome de nevo de Becker

Abstract: Becker nevus syndrome is a phenotype characterized by the fundamental presence of Becker'snevus with ipsilateral hypoplasia of the breast or other skin, skeletal and/or muscular disorders. This syn-drome generally originates at birth, intensifies significantly in adolescence and is one of the syndromes thatconstitute epidermal nevus syndrome. To the best of our knowledge, this is the first case published in theBrazilian literature of Becker nevus syndrome associated with Becker's nevus, ipsilateral breast hypoplasiaand scoliosis in a 14-year-old girl.Keywords: Hamartoma; Hypertrichosis; Nevus; Scoliosis Recebido em 07.05.2009.Aprovado pelo Conselho Consultivo e aceito para publicacao em 27.11.2009. * Trabalho realizado no Instituto de Dermatologia Professor Rubem David Azulay da Santa Casa da Misericordia do Rio de Janeiro - Rio de Janeiro (RJ), Brasil.Conflito de interesse: Nenhum / Conflict of interest : NoneSuporte financeiro: Nenhum / Financial funding : None