Primitive neuroectodermal tumor of the pancreas. Case report and review of the literature

The primitive neuroectodermal tumor of the pancreas, are small round cell tumors arising from the soft tissue that belongs to the family of Ewing's sarcoma, The primary neuroectodermal (PNET) of the pancreas is very rare, have been reported only 17 cases in the literature. We report the case of a 9 year-old female patient, with PNET of the pancreas, was carried out a Whipple surgery, and began chemotherapy treatment with, vincristine, doxorubicin Pegylated, etoposide and ifosfamide and radiation therapy. Currently, the patient is in monitoring since March 2013, with a follow up of 23 months, overall in good condition and without evidence of tumor activity.