Síndrome de bolsa colónica (colon pouch) en el espectro de las malformaciones anorrectales

Congenital colon pouch syndrome, is an infrequent clinical condition in which the colon is totally o partially replaced by a cystic dilatation, and is associated with an anorectal malformation; which may be a urinary tract fistula, a vaginal or vestibule fistula, or a cul-de-sac. We present a rare variant of the anorrectal malformation, with two cases of colon pouch types II and III respectively. The diagnosis was suspected in a plain X-ray and on a distal colostogram. It was confirmed during surgery. The controversial aspects of surgical options are discussed, and emphasis is made on the importance of the follow-up of patients with anorectal malformations, including the need for bowel rehabilitation.