Familial non-syndromic oligodontia

Oligodontia, a rare genetic disorder, represents the congenital absence of more than six teeth in primary, permanent, or both dentitions and is usually the feature of a syndrome. Its occurrence as an isolated entity is even rarer. This article reports non-syndromic oligodontia in two siblings. One case also had concurrent maxillary canine transmigration as one of the rarest associated entities.