Unilateral absence of the pulmonary artery and cavernous transformation of portal vein: a rare combination

A 32-year-old woman was referred to the liver transplant centre, for pretransplant evaluation. Her medical history revealed portal hypertension diagnosed at the age of 6 years, oesophageal varices with history of banding and sclerotherapy by the age of 12 years, as well as multiple episodes of pneumonia. Contrast-enhanced CT of the thorax was performed as part of the routine preoperative workup for liver transplant, which demonstrated unilateral absence of the right pulmonary artery (UAPA) associated with a small right lung and rightward mediastinal shift (figure 1). Additionally, numerous right subpleural cysts were present with diffuse pleural thickening (figure 1). Collateral vessels were noted along the right hemidiaphragm supplied by a single branch coming off the aorta at the level of the coeliac trunk, …