Hybrid Repair of a Thoraco-abdominal Aortic Aneurysm Associated with Polycystic Kidney Disease

Abstract Introduction We report an incidental finding of a 9.8 cm Crawford type III thoraco-abdominal aortic aneurysm associated with autosomal dominant polycystic kidney disease (ADPKD). Case report CT imaging revealed a grossly enlarged polycystic liver and right kidney in a 54-year-old female. The patient had a complex medical history including end-stage renal failure requiring haemodialysis and chronic obstructive pulmonary disease. She had experienced back pain for eighteen months. This was attributed to a progression of pain secondary to abdominal polycystic disease and therefore not investigated. She had previously undergone a left nephrectomy. A single-stage hybrid approach with open retrograde visceral re-vascularisation and endovascular stenting was carried out successfully to treat the aneurysm. Discussion We report this case to highlight the association between aortic aneurysms and ADPKD, and we present a solution to the complex technical problem involved.