Pearls & Oy-sters: Moyamoya Vasculopathy and Its Association With Congenital Heart Disease.

Moyamoya vasculopathy (MMV) is characterized by a progressive, usually bilateral narrowing of the terminal segment of the internal carotid artery or the initial segments of the anterior/middle cerebral artery leading to occlusion and formation of a fragile network of abundant collateral vessels with a high risk of stroke.