A Contribuição da Odontologia no Diagnóstico e Manejo da Síndrome de Sturge-Weber: Relato de dois Casos

Objective: The aim of this study was to report two cases of female patients diagnosed with Sturge-Weber syndrome (SWS), its main oral and maxillofacial clinicals manifestations and dental management. Case report: Case 1. A 30-year-old female patient, referred to the Oral Medicine Clinic of State University of Rio de Janeiro for evaluation of a diffuse reddish lesion over her face and mouth. During the clinical examination, port-wine stains (PWS) were detected on the right side of her face and intraoral discoloration were suggestive of SWS. As the patient referred no symptoms, she was referred to a neurology team to investigate alterations in the central nervous system (CNS). Case 2. A 19-year-old woman was referred for evaluation of a 5-month lasting gingival bleeding in the right mandibular and maxillary alveolar mucosa. Extraoral exam showed the presence of PWS on the right side of her face. Intraorally, the gingival hyperplasia caused malocclusion, plaque deposition and severe bleeding. The SWS diagnosis was established due to these findings. Patient was referred for periodontal treatment. Conclusion: Thus, it is essential that the dentist has knowledge of this condition clinical manifestations in order to do the correct diagnosis and purpose the correct treatment