Persistan Wheezingin Nadir Bir Nedeni: Pulmoner Arter Sling A Rare Cause of Persistent Wheezing: Pulmonary Artery Sling ZKTB

2016 
OZET Giris: Pulmoner arter sling sol pulmoner arterin sag pulmoner arter arka kismindan koken aldigi vaskuler bir patolojidir ve genellikle yasamin ilk yili icinde semptomlar ortaya cikabilir. Olgu: Sekiz aylik erkek cocuk Cocuk Kardiyoloji Poliklinigine duzelmeyen hisilti nedeniyle yonlendirildi. Hastanin hikâyesin- den sikâyetlerinin dogumun birinci ayindan itibaren mevcut oldugu ogrenildi. Hastada persistan wheezing tespit edilmesi nedeniyle kardiyak degerlendirme yapilmasi amaciyla tarafi- miza sevk edildi. Hastanin kardiyak muayenesinde mezokardi- yak odakta 4/6 pansistolik ufurumu mevcuttu. Ekokardiyogra- fide ventrikuler septal defekt, patent duktus arteriozus ve sol pulmoner arterinin sag pulmoner arterden koken aldigi tespit edildi. Hastanin kontrastli toraks tomografisinde sol pulmo- ner arterin sag pulmoner arterden koken aldigi arkaya dogru ilerleyerek trakea ve ozefagus arasindan gecerek sol akciger hilusuna ilerledigi tespit edildi. Trakeanin bu bolgede 3 mm'ye kadar daraldigi izlendi. ABSTRACT Introduction: Pulmonary artery sling is created by anomalous origin of the left pulmonary artery from the posterior aspect of the right pulmonary artery. Symptoms usually occur within the first year of life. Case: Eight-month-old boy was referred to pediatric cardiology department because of persistent wheezing. From the patient's anamnesis the complaints have been found since the first month of life. In order to be detected etiology of persistent wheezing, he was reffered to us due to cardiac evaluation. Pansystolic murmur found in the left lower sternal border on cardiac exa- mination. It was found ventricular septal defect, patent ductus arteriosus and pulmonary artery sling on echocardiography. Chest CT was detected the left pulmonary artery arises right pulmonary artery and then courses behind the trachea and in front of esophagus. Trachea has narrowed up to 3 mm in this region. GIRIŞ
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