Granulomatosis con poliangeitis orbitaria. Agresividad vasculítica

espanolCaso clinico: Mujer de 36 anos con antecedentes de granulomatosis con poliangeitis sin buena adherencia al tratamiento establecido previamente. Se aprecia proptosis, diplopia con alteracion de la abduccion, elevacion y depresion en ojo izquierdo, sin actividad inflamatoria intraocular, ni escleritis. La Resonancia Magnetica Nuclear orbitaria evidencia aumento medial de partes blandas de 3 x 1,2 cm que contacta con el musculo recto interno e inferior secundario a vasculitis activa. Discusion: Cuando la granulomatosis con poliangeitis ocupa la cavidad orbitaria se debe realizar un tratamiento agresivo y explicar la importancia del cumplimiento terapeutico, de otra manera conducira a lesiones irreversibles. EnglishCase report: A 36-year-old woman with personal history of granulomatosis with polyangiitis without good adherence to the treatment previously established. A proptosis, diplopia with impaired abduction, elevation and depression in the left eye without intraocular inflammatory activity and no scleritis are showed. Magnetic resonance imaging evidenced an increased medial orbital soft tissue 3 x 1.2 cm which contacts the inner and inferior rectus muscle secondary to an active vasculitis. Discussion: When granulomatosis with polyangiitis occupies the orbital cavity, an aggressive treatment should be performed, and the importance of adhering to the treatment should be explained, as otherwise it may lead to irreversible damage.