MACRODYSTROPHIA LIPOMATOSA WITH ULNAR DISTRIBUTION IN HAND: MR EVALUATION OF A RARE DISORDER.

Macrodystrophia lipomatosa (MDL) is a congenital progressive gigantism of the hand and foot, which may be local or may involve the entire limb. Macrodystrophia lipomatosa comes to clinical attention mostly because of cosmetic reasons, and rarely due to development of neurovascular compression or mechanical problems like secondary degenerative joint disease. Magnetic resonance imaging (MRI) is considered pathognomonic of MDL and helps to differentiate it from other causes of localized gigantism (1). Although MDL of hand is more common along median nerve distribution; we report a rare case of MDL in a 20 years old female involving ring and little fin gers of right hand with predominant ulnar nerve distribution.