Supravalvular Stenotic Mitral Ring with Ventricular Septal Defect

Background: Supravalvular mitral ring is exceedingly uncommon. Methods: We report a 4-year-old girl with supravalvular stenotic mitral ring and ventricular septal defect (VSD). The VSD was closed by a Dacron patch and the supravalvular ring was excised. For treatment of supravalvular mitral ring with obstruction, surgical resection is commonly performed. Results: There are no reports of long-term follow-up after resecting the supravalvular mitral ring. Conclusion: In our case, no mitral stenosis was evident on postoperative echocardiogram performed 3 years after surgery.