542 Descriptive Analysis of the Immunological Behavior of Patients with Ataxia Telangiectasia Attended in the National Institute of Pediatrics in the Past 30 Years.

Background Ataxia Telangiectasia is an autosomal recessive disease characterized by progressive neurological impairment, ataxia, oculo-cutaneous telangiectasia, immunodeficiency, recurrent infections sinopulmonary and cancer predisposition processes. It does not exist in clinical practice guidelines for boarding and management of these patients, neither a suggestion of monitoring.