Bronchopulmonary foregut malformations presenting as mass lesions in children: spectrum of imaging findings.
2008
153 B ronchopulmonary foregut malformations (BPFMs), also known as congenital lung malformations or abnormalities, are a heterogeneous group of disorders involving conducting airways, lung parenchyma, and lung vasculature. Several malformations that present as mass lesions have been described, some of which include bronchogenic cyst (BC), pulmonary sequestration (PS), congenital cystic adenomatoid malformation (CCAM) [currently named as congenital pulmonary airway malformation (CPAM)], congenital lobar emphysema (CLA) [currently named as congenital lobar overinflation (CLO)], bronchial atresia, and congenital pulmonary cyst (CPC) (1–4). Moreover, combinations of those malformations (hybrid malformations) have also been described (2, 5–7). These malformations can manifest in various ways from respiratory distress at birth to incidental findings on chest radiograph. Although malignancies have been described with BPFMs, the number of reported cases is less than fifteen (8).
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