Stickler's syndrome and neovascular glaucoma.

SUMMARY A case ofStickler's syndrome with neovascular glaucoma is described. Wagner (1938) described a Swiss family withdominantly inherited vitreoretinal degeneration,and von Bohringer et al. (1960) re-examined thefamily, adding further members. The characteristicfindings which Wagner described were an optically empty vitreous with peripheral avascular mem- branes, peripheral visual field constriction, narrow- ing and sheathing of the peripheral retinal arterieswith pigment clumping adjacent to the abnormalvessels and elsewhere in the periphery, choroidalvascular sclerosis and atrophy, myopia, and discpallor in advanced cases. Presenile posterior sub-capsular cataracts were present in some patientswhile in others these had become mature. None ofthe patients described by Wagner ('1938) andsubsequently by von Bohringer and others (1960) were reported to have retinal detachment, and yet further families have been described in whom therisk of retinal detachment was high and the resultsof