Tumor desmoide: reporte de un caso

El tumor desmoide es una neoplasia rara de tejidos blandos que se desarrolla a partir de musculo, tejido conectivo, fascia y aponeurois. Se presenta esporadicamente y mas frecuentemente en mujeres. El caso que se presenta concierne a paciente femenina de 27 anos que fue sometida a escision radical de una gran masa que infiltraba musculo recto abdominal, diagnosticada como tumor desmoide. Aunque tiene caracteristicas benignas, es de naturaleza infiltrativa y se comporta como una masa localmente agresiva, la cual puede invadir estructuras adyacentes haciendo que la reseccion quirurgica sea dificil. El unico tratamiento viable es la cirugia amplia dejando bordes sanos, esto causa gran defecto de pared y por tanto serios problemas en la reconstruccion. Ademas, la tasa de recurrencias locales varia y depende de la edad del paciente, localizacion y los margenes de reseccion.(AU) Desmoid tumor is quite rare soft tissues neoplasm that develops from muscle connective tissue, fasciae and aponeuroses. This neoplasm occurs in sporadic and more frequent in women than men. The presented case report refers to young female (27 years old), who underwent the radical excision of a large desmoid tumour infiltrating the right rectus muscle of the abdomen. Although desmoid is classified pathologically as a benign tumour, its infiltrative nature leads to a locally aggressive mass, which can invade surrounding structures and organs making surgical resection difficult. The only radical treatment for her was the surgical resection carried out far from the tumour borders into the healthy tissues. This resection causes wide muscle-fascial defects determining serious reconstructive problems. Futhermore, overall local recurrence rates vary and depend on patient’s age, tumour location and margins at resection.(AU)