Leiomiosarcoma intraóseo mandibular

2007 
espanolLos leiomiosarcomas son neoplastias malignas mesenquimales derivadas del musculo liso. Los leiomiosarcomas intraoseos mandibulares primarios son muy raros. Se cree que proceden de la musculatura lisa de la pared de los vasos sanguineos. Pueden presentarse a cualquier edad, sin ninguna predileccion y afectan preferentemente a hombres, con una relacion hombre-mujer de 2:1. La excision quirurgica completa esta asociada con una menor recidivia y mayor supervivencia. La radioterapia es efectiva en el tratamiento de la enfermedad miucrsocopica residual. Presentamos el caso de un leiomiosarcoma intraoseo mandibular. EnglishLeiomyosarcomas are malignant mesenchymal neoplasm of smooth muscle dfferentiation. Leiomyosarcomas occurring in the jawbones are exceedingly rare, and are believe to arise from the musculature of the tunica of blood vessels. Intraoral cases may present at any age with no predilection for any age group. They occur predominantly in males, with a male to female ratio of approximately 2:1. Complete surgical excision is associated with low recurrence and longer survival. Radiotheraphy is effective in the treatment of microscopic disease.
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