Huge primary retroperitoneal mucinous cystadenoma of borderline malignancy mimicking an ovarian mass: Case report and review

Background: Primary retroperitoneal mucinous cystadenoma:isararetumoronly 48caseshavebeenreported in international literature. Patients affected by primary retroperitoneal mucinous cystadenoma/cystadenocarcinoma rangedinagefrom17to86years(median,42.3years)andthe size of the cystis ranged from 5 to 35 cm (median, 16.1 cm). There is no unanimous opinion on the genesis of these tumors and, due to the ir extreme rarity, its histogenesis, biological behavior and the optimal management strategy remain at a speculative level. Case report: We report the case of a huge borderline primary retroperitoneal mucinous cystadenoma (24 ◊25cm)ina35-year-oldwomanandthestrategiesadopted for the diagnosis and surgical management. Conclusion: Primary mucinous cystic tumor of the retroperitoneum was correctlydiagnosedonlyatthetimeofsurgery.Aswellasinthe majority of cases reported in the literature, preoperative investigationswerenotabletogiveinformationaboutthetumor site. In spite of the short follow-up (two years), the patient's favorable course supports the hypothesis that primary retroperitoneal mucinous cystadenoma may be treated in the same manner as a primary ovarian tumor of the same grade andcomparablestage. Primary retroperitoneal mucinous cystadenoma (PRMC), arising within the retroperitoneal space but outside the major organs within that compartment, is rare. Regarding cystadenoma or cystadenocarcinoma in the retroperitoneum, 48caseshavebeenreportedininternationalliterature(TableI)