Tumor-like appearance in ruptured sinus of Valsalva with quadricuspid aortic valve

Abstract Sinus of Valsalva rarely ruptures due to congenital causes. When it comes to ruptured sinus of Valsalva combined with quadricuspid aortic valve, no cases have so far been reported in Japan. Here, we describe the case of 32-year-old female who developed ruptured sinus of Valsalva with tumor-like appearance. Some of the cases of ruptured sinus of Valsalva show aorta to right atrial tunnel with a windsock aneurysm looking like a tumor by echocardiography. Learning objective: Sinus of Valsalva rarely ruptures due to congenital causes such as aortic valve anomalies such as quadricuspid aortic valve. Ruptured sinus of Valsalva sometimes shows tumor-like appearance by echocardiography. In such a case, we need to keep in mind that the sinus of Valsalva with aortic valve anomalies rarely ruptured showing a fistulous pouch-like “windsock” in the edge of aneurysm by echocardiography.>