Cerebral angiomatosis: Report of a case in an infant, with a review of the literature

Summary The clinical history and autopsy findings are presented in a child with cerebral angiomatosis. The pertinent literature has been reviewed. General symptoms and signs of such lesions are paresis, epilepsy or convulsions, hemorrhage, less commonly chronic headache, mental deterioration, cranial bruits, visual field defects, diplopia due to sixth nerve paralysis, and symptoms secondary to increased intracranial pressure. Final diagnosis usually can be made by intracranial angiography. The treatment of choice is radical surgical excision or obliteration and should be carried out whenever feasible. The value of intracranial arterial ligation or incomplete removal of the anomaly may be questioned. Radiation is of no value.