Updates on Recent Developments in Idiopathic Intracranial Hypertension

Idiopathic intracranial hypertension (IIH) or pseudotumor cerebri syndrome (PTCS) is a condition in which the intracranial pressure is increased without radiographic or laboratory evidence of intracranial pathology or localizing neurological signs, with the exception of papilledema and/or a cranial nerve VI palsy. As the pathophysiology of IIH is not well understood, current treatment strategies center on managing symptoms and preventing morbidity. This review aims to provide an updated overview on typical and atypical presentations, diagnostic criteria, work up, treatment options, and current theories on the pathophysiology of IIH.