Persistent fetal vasculature with microphakia, lacrimal drainage disorder, and congenital ptosis: An unusual presentation

Persistent fetal vasculature (PFV) is a rare congenital ocular anomaly, characterized by failure of regression of embryonal hyaloid vasculature and is known to cause a broad range of anomalies. We report a 3-month old female infant with PFV, congenital nasolacrimal duct obstruction, and congenital ptosis in the left eye. At the time of lens aspiration, microphakia was seen after dilatation with a Malyugin ring. The child underwent uneventful lens aspiration, primary posterior capsulotomy, and anterior vitrectomy. All these features point towards role of abnormal embryological development in PFV. The meticulous surgical technique is essential to prevent intraoperative and postoperative complications in these patients.