No association of the hypercoagulable state with sickle cell disease related pulmonary hypertension

Pulmonary hypertension (PHT) occurs in approximately 30% of adult patients with sickle cell disease (SCD) and is a risk factor for early death.[1][1] Hypercoagulability has been linked to PHT in general and pulmonary artery thrombosis contributes to PHT progression regardless of its cause.[2][2]