HUGHES-STOVIN SYNDROME: AN INCOMPLETE BEHCET'S DISEASE

Hughes Stovin syndrome is very uncommon condition characterized by deep vein thrombosis (DVT) and pulmonary artery aneurysm. The etiology is still not known but it is considered to be manifestation of systemic vasculitis. It shares many clinical signs and symptoms with Behcets disease and that is why it is also called incomplete Behcets disease or variant of it. Here we report a male patient case who presented to our tertiary care hospital with DVT and pulmonary artery aneurysm. CT angiography showed aneurysmal dilatations of segmental and sub segmental pulmonary arteries.  He was successfully treated with steroids and immunosuppressant. Key Words: Aneurysm; Behcets syndrome; Pulmonary artery; Venous thrombosis.