WDHA syndrome by composite pheochromocytoma and ganglioneuroma

Atsushi Ishiguro,Yuichi Hirai,Noriyuki Hasegawa,Junko Nakamura,Michiko Tamura,Shouji Nishimura,Mitsuomi Kaimori,Hironobu Sasano

WDHA syndrome by composite pheochromocytoma and ganglioneuroma

2002

Atsushi Ishiguro
Yuichi Hirai
Noriyuki Hasegawa
Junko Nakamura
Michiko Tamura
Shouji Nishimura
Mitsuomi Kaimori
Hironobu Sasano

症例は51歳,男性.水様性下痢,四肢脱力で近医受診.低K血症,右副腎腫瘍を認め当科紹介となった.血中vasoactive intestinal polypeptide (VIP),血中・尿中カテコラミンおよびその代謝産物の高値を認めwatery diarrhea-hypokalemia-achlorhydria (WDHA)症候群を呈した褐色細胞腫と診断.腫瘍摘出術後,臨床症状,各種検査値の改善が得られた.病理組織像より,褐色細胞腫・神経節腫混合腫瘍でVIP分泌は神経節腫部由来と判明した.

Keywords:

Pheochromocytoma
WDHA Syndrome
Pathology
Ganglioneuroma
Diabetes mellitus
Medicine

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