Progressive systemische Sklerodermie und Schwangerschaft

: Progressive systemic sclerosis is a connective tissue disease with inflammation and fibrosis. Pregnant women with progressive systemic sclerosis have an increased risk for preterm births and probably for small-for-date babies. We report the case of a 28-year-old II G O P suffering from progressive systemic sclerosis with severe pulmonary fibrosis and affection of the oesophagus. She was admitted to hospital at 32 weeks of gestation with premature labour and cervical incompetence. At 34 weeks of gestation she was delivered by Caesarean section with spinal anaesthesia because of foetal growth arrest and decreased pulmonary function. The operation and the postoperative course were without any complications. Pregnant women with progressive systemic sclerosis have an increased risk for renal and pulmonary complications (hypertension, hypoxia). Therefore careful interdisciplinary obstetric monitoring is very important.