GP241 Neonatal outcomes for babies with ebstein’s anomaly

2019 
Introduction Ebstein’s anomaly is a rare form of congenital heart disease (CHD), occurring in less than 1% of patients with CHD.With advances in Fetal Medicine and Cardiology, Ebstein’s anomaly is being diagnosed antenatally. The literature highlights that it can be difficult to predict the prognosis particularly during the neonatal period. Our aim was to review the neonatal outcomes of babies with Ebstein’s anomaly admitted to our tertiary neonatal intensive care unit (NICU). Methods We retrospectively identified all babies admitted to the NICU with a documented diagnosis of Ebstein’s anomaly between 01/04/2009 and 01/04/2018. Their outcome data was collected using electronic records (BadgerNet® and HeartSuite). Results In the last 9 years, ten babies had a documented diagnosis of Ebstein’s anomaly. Nine of these were antenatally diagnosed. Four were born prematurely ( Conclusions In our experience, Ebstein’s anomaly was fatal in babies born prematurely. The term babies had improved survival but even this was only 50%. The outcomes in the neonatal period can vary significantly for babies with this diagnosis as highlighted in our case series. Although the numbers are small due to the high mortality rates in this group, it is important that parents are counselled appropriately antenatally so that they are adequately prepared for the poor outlook of babies born with Ebstein’s anomaly.
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